The context of Bernard - Soulier syndrome & it's culmination in the demense of prosthodontics
BSS - A Prosthodontic perspective
Abstract
Bernard – Soulier syndrome is a rare hereditary disorder with giant cell platelets, thrombocytopenia and extended bleeding time. In thrombosis and hemostasis, platelets play a main role. The first stage in the creation of hemostatic plugs is the accumulation of platelets at the site of vascular injury that plays a key role in stopping the blood loss following the injury. The genetic error is induced by the glycoprotein complex lb/IX/V, which is the Von Willebrand factor on the platelet surface. Here we are reporting a 78 year old male patient which comes with chief complaint of missing teeth, root stumps & worn out teeth in upper and lower arches, inability to chew properly and wants replacement for the same. The primary treatment remains platelet transfusion pre & post extraction. Root canal treatment was performed on remaining natural teeth. Conventional over denture prosthesis for upper arch and dolder bar attachment overlay denture was fabricated for the lower arch.
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