Oral - Systematic manifestation of Bardet- Biedl Syndrome: A rare case report from Jaipur, Rajasthan

Oral - Systematic manifestation of Bardet- Biedl Syndrome

  • Dr Debopriya Chatterjee Rajasthan University of Health Sciences
  • Dr. Anjali Kapoor
  • Dr Sanjeev Choudhary
  • Dr Meenakshi Sharma
Keywords: Bardet Biedl Syndrome, Dental anamolies

Abstract

Bardet Biedl Syndrome (BBS) is a rare, heterogenous, ciliopathic autosomal recessive condition, affecting multiple organs. Primary features include polydactyly, obesity, mental retardation, hypogonadism, retinopathy and renal failure. Dental anomalies is regarded as secondary features, include hypodontia, microdontia, short roots and deep palate. Less than 15 cases have been reported from India. This article reports a case of Bardet- Biedl Syndrome in a male with typical systemic and oral features. This case exemplifies the need of multidisciplinary approach.

Published
2021-06-10
How to Cite
Chatterjee, D. D., Kapoor, D. A., Choudhary, D. S., & Sharma, D. M. (2021). Oral - Systematic manifestation of Bardet- Biedl Syndrome: A rare case report from Jaipur, Rajasthan. UNIVERSITY JOURNAL OF DENTAL SCIENCES, 7(2). https://doi.org/10.21276//ujds.2021.7.2.18